Region Jnkpings ln Odontologiska Institutionen

Early dental treatment of a boy with hypohidrotic ectodermal dysplasia and oligodontia – a case report

Norderyd J*, Bergendal B


Oral habilitation in young children necessitates consideration not only of the dental and oral conditions but also of the growing child's physical and psychological development. The aim here is to describe the dental treatment given to a small child with hypohidrotic ectodermal dysplasia and oligodontia.

Materials and methods

A boy, 2 years 9 months old, was diagnosed with hypohidrotic ectodermal dysplasia and multiple tooth agenesis in both dentitions. In addition, he had feeding problems, easily triggered gagging reflexes, and language difficulties. Since he was of foreign origin, he didn't speak or understand the language spoken by the care-givers. He was too immature to accept dental treatment. Two years later he was diagnosed with ADHD. Treatment was planned by a multidisciplinary team of specialists in paediatric dentistry, prosthodontics, and orthodontics. The first 2 years of treatment are described.


The boy was thoroughly examined clinically and radiographically under general anaesthesia, and the malformed upper cuspids were reshaped with composite resin material. Impressions were also taken. At the age of 2 years and 10 months, the boy received a denture in the upper jaw. The parents reported after treatment that apart from enhanced appearance, biting and chewing also improved. The denture was continuously monitored and altered as the boy grew and the upper primary second molars erupted. Impressions for a new denture were taken under rectal sedation with midazolam when the child was 3 years and 9 months old. The different aspects of treatment were successful, and the boy has continued dental treatment in his home country.


A multidisciplinary team approach and early treatment start are beneficial in oral habilitation of oligodontia. Since it is as important to avoid dental fear as well as to give the child good oral function and appearance, behaviour management methods in combination with the use of sedation and pain control are essential.

Uppdaterad: 2013-04-03
Anna Thofelt, Avdelningen för odontologisk radiologi Jönköping, Folktandvården