Region Jnkpings ln Odontologiska Institutionen

A dental management protocol for Amelogenesis Imperfecta - report from a workshop

Norderyd J, Bergendal B


Amelogenesis Imperfecta (AI) is a general hereditary enamel disturbance that is characterised by clinical and genetic heterogeneity. It can be divided in three main groups, hypoplasia, hypomaturation, and hypocalcification types of AI. AI can be a severe disability to the growing individual and dental management can be very difficult. The aim was to make a dental management protocol for AI.


A group of Swedish specialists in orthodontics, paediatric dentistry, and prosthodontics were invited to a two-day workshop in January 2006, in order to establish guidelines for dental management of AI. The participants were B Bergendal, B Bäckman, C Göthberg, E Josefsson, A Lindunger, B Mohlin, J Norderyd, S Scholander, and S Sundell. Available literature was studied before the meeting and this, together with the clinical experience of the workshop participants, was the base for the discussion.


A dental management protocol concerning young patients with AI was agreed upon. The guidelines are general, since specific treatment decisions have to be adapted to the patient's dental and oral status as well as to the individual's physical and psychological development. The aim is to assure that the patient is given adequate treatment at the right time and that treatment planning is made early and with recurrent intervals by a multidisciplinary group of specialists. Recommended treatment goals are stated together with clinical examples with reference to the primary, mixed, and permanent dentitions respectively. The dental management protocol can be found at


When a general enamel mineralisation disturbance is suspected, the child should be referred to a specialist in paediatric dentistry for further diagnostics and treatment planning. When it concerns rare disorders guidelines are important for assuring quality in care.

Uppdaterad: 2013-04-03
Anna Thofelt, Avdelningen för odontologisk radiologi Jönköping, Folktandvården